Desmoplastic Small Round Cell Tumors (DSRCT) Diagnosis

Desmoplastic small round cell tumors (DSRCTs) are so rare that they are often overlooked as the root of disease. Sometimes, patients will come to MSK thinking they have one type of cancer, but our precise testing will indicate that they actually have a different type. Because our team of pathologists only sees patients with cancer, they are experts at identifying both defining characteristics and subtle nuances of each disease.

Analyzing a sample of the patient’s tumor can reveal the unique genetic marker found only in DSRCTs. This can help doctors make a correct diagnosis. Although DSRCTs most commonly occur in the abdomen, they can appear in any part of the body.

DSRCTs can spread widely throughout the body. Our experts often examine patients’ bone marrow and do imaging studies — such as CT, MRI, and PET — to determine how far the cancer has spread.

Our doctors treat DSRCTs based on their stage, or how far the tumor has spread. Staging helps determine the treatment plan used for each patient with DSRCT.